Product Name :
Sarcoglycan-β (V136) Peptide Applications :
Blocking Background :
Four sarcoglycan subunit proteins, designated α-, β-, γ- and δ-sarcoglycan, form a complex on the skeletal muscle cell surface membrane. A genetic defect in any one of these proteins causes the loss or marked decrease of the whole sarcoglycan complex, which is observed in the autosomal recessive muscular dystrophy, sarcoglycanopathy. In smooth muscle, β- and δ-sarcoglycans are associated with ε-sarcoglycan, a glycoprotein homologous to α-sarcoglycan. Additionally, a complete deficiency in δ-sarcoglycan is the cause of the Syrian hamster BIO.14 cardiomyopathy. Alternative Name :
SGCB; 43DAG; A3B; BETA-SARCOGLYCAN; BETA-SG; LGMD2E; SGC Swiss-Prot :
Q16585 Product :
1 mg/ml in DI water. Purification&Purity :
Synthetic peptide Sarcoglycan-β (V136). (Note: the amino acid sequence is proprietary). The purity is > 98%. Storage&Stability :
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles. Specificity :
This peptide can be used with studies using BS3518 Sarcoglycan-β (V136) pAb.
Sarcoglycan-β (V136) Peptide Applications :
Blocking Background :
Four sarcoglycan subunit proteins, designated α-, β-, γ- and δ-sarcoglycan, form a complex on the skeletal muscle cell surface membrane. A genetic defect in any one of these proteins causes the loss or marked decrease of the whole sarcoglycan complex, which is observed in the autosomal recessive muscular dystrophy, sarcoglycanopathy. In smooth muscle, β- and δ-sarcoglycans are associated with ε-sarcoglycan, a glycoprotein homologous to α-sarcoglycan. Additionally, a complete deficiency in δ-sarcoglycan is the cause of the Syrian hamster BIO.14 cardiomyopathy. Alternative Name :
SGCB; 43DAG; A3B; BETA-SARCOGLYCAN; BETA-SG; LGMD2E; SGC Swiss-Prot :
Q16585 Product :
1 mg/ml in DI water. Purification&Purity :
Synthetic peptide Sarcoglycan-β (V136). (Note: the amino acid sequence is proprietary). The purity is > 98%. Storage&Stability :
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles. Specificity :
This peptide can be used with studies using BS3518 Sarcoglycan-β (V136) pAb.
Blocking peptide available as BS3518PP